Bronchiolitis Obliterans Organizing Pneumonia
National Organization for Rare Disorders, Inc.
It is possible that the main title of the report Bronchiolitis Obliterans Organizing Pneumonia is not the name you expected.
Bronchiolitis obliterans organizing pneumonia (BOOP) is a rare inflammatory lung disorder. Symptoms of BOOP vary greatly from case to case and may include a persistent cough, flu-like illness, and difficult breathing upon exertion (dyspnea). The term bronchiolitis obliterans refers to the accumulation of masses or plugs of fibrous, granulation tissue that forms in the small airway tubes of the lungs (bronchioles) blocking (obliterating) the flow of air. Organizing pneumonia refers to the peculiar, distinct organization of the cells of the air sacs (alveoli) and air ducts (alveolar ducts) and accompanying in inflammation of the lungs (pneumonia). Individuals with BOOP experience inflammation of the bronchioles and air sacs simultaneously, which distinguishes it from other similar inflammatory lung disorders.
Although several different known causes of BOOP have been identified, most cases occur for no known reason (idiopathic). Idiopathic BOOP may also be called cryptogenic organizing pneumonia. Some researchers prefer the use of COP to avoid confusion with other lung disorders with similar names. The term cryptogenic denotes that the cause of the disorder is unknown. Other researchers prefer the term BOOP because it the most recognized term for the disorder.
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This is an abstract of a report from the National Organization for Rare Disorders, Inc. ® (NORD). A copy of the complete report can be obtained for a small fee by visiting the NORD website. The complete report contains additional information including symptoms, causes, affected population, related disorders, standard and investigational treatments (if available), and references from medical literature. For a full-text version of this topic, see http://www.rarediseases.org/search/rdblist.html