Heart Block, Congenital
National Organization for Rare Disorders, Inc.
It is possible that the main title of the report Heart Block, Congenital is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.
- First Degree Congenital Heart Block
- Second Degree Con. Heart Block (Wenckebach [Mobitz I]; Mobitz II; included)
- Third Degree Congenital (Complete) Heart Block
Congenital heart block is characterized by interference with the transfer of the electrical nerve impulses (conduction) that regulate the normal, rhythmic, pumping action of the heart muscle (heart block). The severity of such conduction abnormalities varies among affected individuals.
The normal heart has four chambers. The two upper chambers are the atria and the two lower chambers are the ventricles. Within the right atrium of a normal heart is a natural pacemaker that initiates and controls the heartbeat. The electrical stimulus travels from the pacemaker (sinoatrial or SA node) to the ventricles along a very specific path consisting of conducting tissue and known as the AV (atrioventricular) node. As long as the electrical impulse is transmitted normally, the heart behaves normally.
If the transmission of the signal is impeded, the blocked transmission is known as a heart block or an AV block. If the heart block occurs in the fetus or newborn, the condition is known as congenital heart block. This condition has nothing at all to do with the flow of blood or with the blockage of a major or minor coronary artery. It is an electrical problem rather than a hydraulic one.
Heart blocks are categorized according to the degree of impairment of the patient. The categories are first, second and third degree heart block
American Heart Association
7272 Greenville Avenue
Dallas, TX 75231-4596
Congenital Heart Anomalies, Support, Education, & Resources, Inc. (CHASER, Inc.)
2112 North Wilkins Road
Swanton, OH 43558
International Bundle Branch Block Association
6631 West 83rd Street
Los Angeles, CA 90045-2875
NIH/National Heart, Lung and Blood Institute
31 Center Drive MSC 2480
Building 31A Rm 4A16
Bethesda, MD 20892-2480
Kids With Heart National Association for Children's Heart Disorders, Inc.
P.O Box 12504
Green Bay, WI 54307-2504
Little Hearts, Inc.
P.O. Box 171
110 Court Street, Suite 3A
Cromwell, CT 06416
Congenital Heart Information Network (C.H.I.N.)
101 N Washington Ave, Suite 1A 101 N Washington Ave, Suite 1A
Margate City, NJ 08402-1195
MUMS National Parent-to-Parent Network
150 Custer Court
Green Bay, WI 54301-1243
Genetic and Rare Diseases (GARD) Information Center
PO Box 8126
Gaithersburg, MD 20898-8126
Fetal Hope Foundation
9786 S Holland Street
Littleton, CO 80127
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This is an abstract of a report from the National Organization for Rare Disorders, Inc. ® (NORD). A copy of the complete report can be obtained for a small fee by visiting the NORD website. The complete report contains additional information including symptoms, causes, affected population, related disorders, standard and investigational treatments (if available), and references from medical literature. For a full-text version of this topic, see http://www.rarediseases.org/search/rdblist.html